内容概况：近年来，PDH技术在催化剂、反应工艺和设备效率等方面不断优化，使得投资成本降低、能耗减少。伴随政府大力 ...

Defects in the oxidative phosphorylation (OXPHOS) system — the final biochemical pathway in the production of ATP — result in devastating, mainly multisystem diseases. The OXPHOS system is ...