Sometimes children with heterotaxy syndrome have dextrocardia syndrome. This means the heart is in the right chest instead of the left chest. Here are general descriptions of two types of heterotaxy syndrome.

Example of the types of heart defects seen in heterotaxy: dextrocardia, complete atrioventricular canal defect, double outlet right ventricle, pulmonary stenosis, and interrupted inferior vena cava.

Heterotaxy syndrome (HS) constitutes a spectrum of anomalies arising from embryological errors that result in abnormalities of lateralization involving thoraco-abdominal viscera and culminate in loss of normal asymmetric arrangement of these organs.

Dextrocardia with heterotaxy In dextrocadia with heterotaxy syndrome, some or all of the vital organs are misplaced, or not in their normal positions in the body. Certain organs may be absent or only partially developed.

Heterotaxy, also known as situs ambiguus, is the term used to describe the abnormality in left-right laterality in overall whole-body patterning. Heterotaxy differs from both normal visceral arrangement (situs solitus) and the mirror-image of organ anatomy (situs inversus).

What is heterotaxy syndrome? Heterotaxy syndrome is a rare condition in which some of the body’s organs may be in an abnormal place or formed abnormally, and may not work the right way. The organ systems most commonly affected are the heart, lungs, immune system and the gastrointestinal (GI) tract.

Heterotaxy syndrome affects every child differently. Symptoms may be mild or severe, depending on the complexity of the heart defects and problems in other organs. Infants with significant heart defects have symptoms soon after birth, such as:

Heterotaxy syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the womb. This can result in many different organ systems being affected, and also means that each individual with heterotaxy is unique.

The term heterotaxia or heterotaxy refers to a complex syndrome of congenital defects affecting the organs of the abdomen and chest. Other names used to describe this spectrum of disorders are cardiosplenic syndrome, Ivemark’s syndrome, and right (or left) atrial isomerism.

2022年5月10日 · Many people with dextrocardia have an additional congenital syndrome including: Heterotaxy: This condition causes mirrored organs in your chest and abdomen. But those organs aren’t formed properly or don’t work as they should.