Sarcoma botryoides or botryoid sarcoma [1] is a subtype of embryonal rhabdomyosarcoma, that can be observed in the walls of hollow, mucosa lined structures such as the nasopharynx, common bile duct, urinary bladder of infants and young children or the vagina in females, typically younger than age 8.

2024年8月30日 · Embryonal rhabdomyosarcoma (ERMS) is the most common subtype of RMS, occurring in soft tissue and visceral sites of young children, and is associated with favorable outcomes. A subset occurs in mucosal-lined luminal structures, displaying a unique grape-like growth termed as "botryoid-type." To furt …

2022年3月3日 · Botryoid embryonal rhabdomyosarcoma (sarcoma botryoides) only occurs in certain locations, specifically beneath mucosal epithelial lined viscera, such as the bladder, biliary tract, vagina or upper respiratory tract, extrahepatic …

2024年12月1日 · We report the case of a 2-year-old girl who presented with a rapidly growing mass in the vulvar region. A pelvic MRI revealed a grape-like mass occupying the vaginal lumen, suggestive of botryoid rhabdomyosarcoma. Biopsy of the mass confirmed the diagnosis.

Gross Pathology: Botryoid rhabdomyosarcoma (RMS) has a characteristic polypoid, grape-like gross appearance (botryoid = Greek for bunch of grapes). It is usually found in mucosa-lined hollow viscera such as urinary bladder, vagina, nasal cavity, nasopharynx, and the common bile duct. The specimen shown here involved the nasopharynx.

2025年2月4日 · Specifically, sarcoma botryoides is a variant of embryonal rhabdomyosarcoma that is characterized by the presence of a round, grape-like mass in the affected organ. Sarcoma botryoides most commonly affects individuals under the age of 4, although it can sometimes occur in older individuals.

2024年6月16日 · Sarcoma botryoides is a rare and aggressive type of embryonal rhabdomyosarcoma, a malignant tumor that arises from primitive muscle cells. It most commonly affects the vagina and bladder in young children and infants. Rhabdomyosarcoma is the most common soft tissue sarcoma in children, accounting for 4-6% of all pediatric cancers.

2024年11月28日 · Lesions can be large. Signal characteristics are similar to rhabdomyosarcoma i.e 1: T1: low to intermediate. T2: high. Grapelike intraluminal masses would favour a botryoides type. History and etymology. Botryoid, derived from the Greek bótry(s) for grape, means resembling the form of grapes. Differential diagnosis

choledochal stones, and choledochal malformation (choledochal cyst). The botryoid variant, with its typical grape-like growth pattern, is the most frequent form of rhabdomyosarcoma affecting the biliary tract. Being a highly chemosensitive tumor, its prognosis has greatly improved in recent years, relegating surgery to a secondary role.

Botryoid rhabdomyosarcoma is an aggressive malignancy that arises from embryonal rhabdomyoblasts. It is commonly seen in the genital tract of female infants and young children. Due to the young age of affected patients, this malignancy poses a management challenge as the preservation of hormonal, sexual and reproductive function is essential.