2009年4月14日 · The Birmingham EB Severity (BEBS) score was tested on 97 patients aged 0–64 years. Results Eleven items were scored: area of damaged skin, involvement of nails, mouth, eyes, larynx and oesophagus, scarring of hands, skin cancer, chronic wounds, alopecia and nutritional compromise.

The Birmingham EB Severity (BEBS) score was tested on 97 patients aged 0-64 years. Results: Eleven items were scored: area of damaged skin, involvement of nails, mouth, eyes, larynx and oesophagus, scarring of hands, skin cancer, chronic wounds, alopecia and …

Epidermolysis bullosa (EB) is a diverse group of hereditary blistering disorders encompassing four major forms, simplex (EBS), junctional (JEB), dystrophic (DEB) and Kindler syn-drome, as well as numerous subtypes.1 EB ranges in severity from occasional …

Results: Total EBDASI score ranges of 0-42, 43-106 and 107-506 corresponded to mild, moderate and severe disease respectively. Reduction in EBDASI activity scores of greater than 9 indicated clinically significant improvement. An increase of …

An accurate diagnosis is essential for managing and counselling patients with EB. The latest EB classification lists more than 30 subtypes and high levels of clinical and laboratory expertise are required to differentiate them.

EB comprises four main types: EB simplex (EBS), junctional EB (JEB), dystrophic EB (DEB) and Kindler syndrome (KS), with more than 30 clinical subtypes (Tables 2 and 3). EB is clinically heterogeneous, including a broad spectrum of severity.

2009年5月1日 · Objectives To develop a severity score covering all subtypes of EB at all ages that is simple, valid, sensitive and reliable. Methods Score items and weightings were generated by expert consensus, and refined for content and face validity. The Birmingham EB Severity (BEBS) score was tested on 97 patients aged 0–64 years.

The final score, Instrument for Scoring Clinical Outcome of Research for Epidermolysis Bullosa (iscorEB), is a combined score that contains clinician items grouped in five domains (skin, mucosa, organ involvement, laboratory abnormalities, and complications and procedures; maximum score 114) and patient-derived items (pain, itch, functional ...

2009年6月1日 · EB severity was evaluated following the Birmingham epidermolysis bullosa severity (BEBS) score, which includes not only the area of skin damage but also nail and mucosal...

大疱性表皮松解症(EB )是一组有差异的遗传性大疱性疾病,包括四大类,单纯型(EBS),交界型(JEB ),营养不良型(DEB )和金德乐综合征,有很多亚型。 EB的严重程度 跨越从偶尔因摩擦起水疱到广泛和致死性的疾病。