Repeat bronchoscopy can be useful in the early recognition of IPH, especially in the case of retained opacities after AH on HRCT. IPH can induce insidious pulmonary fibrosis. The exact aetiology, incidence, and prevalence are unknown, but 80% of …

2023年7月24日 · Idiopathic pulmonary hemosiderosis (IPH) is a rare disease characterized by repeated episodes of a diffuse alveolar hemorrhage resulting in the accumulation of hemosiderin inside pulmonary macrophages. Early recognition and prompt diagnosis can help reduce the high morbidity and mortality associated with this condition.

2019年7月17日 · While several interstitial diseases have been diagnosed by histopathological analysis of cryobiopsy samples, there are no studies, which would refer to idiopathic pulmonary hemosiderosis (IPH) confirmed by this diagnostic method. Here, we present what we believe to be the first IPH case to be confirmed by TLCB.

Idiopathic pulmonary haemosiderosis (IPH) is a lung disease of unknown cause that is characterized by alveolar capillary bleeding and accumulation of haemosiderin in the lungs. It is rare, with an incidence between 0.24 [1] and 1.23 [2] cases per million people.

2021年1月1日 · Idiopathic Pulmonary Hemosiderosis (IPH) is a rare cause of diffuse alveolar hemorrhage (DAH). IPH is characterized by recurrent episodes of DAH without any identifiable etiology, such as infection, Goodpasture syndrome, anti-neutrophil cytoplasmic antibody (ANCA) associated vasculitis (AAV) and other rheumatologic diseases.

Idiopathic pulmonary hemosiderosis is a rare disorder that can occur at any age and is characterized by the triad of hemoptysis, iron deficiency anemia and diffuse pulmonary infiltrates. The clinical course is exceedingly variable especially in children and a substantial proportion of this age group is undiagnosed.

2013年10月14日 · Idiopathic pulmonary hemosiderosis (IPH) is a rare cause of alveolar hemorrhage in children and its pathophysiology remains obscure. Classically, diagnosis is based on a triad including hemoptysis, diffuse parenchymal infiltrates on chest X-rays, and iron-deficiency anemia.

2022年10月5日 · Idiopathic pulmonary hemosiderosis (IPH) is a rare lung disease, mostly affecting children under 10 years old. “Idiopathic” means the cause is not yet known, “pulmonary” refers to involvement of the lungs, and “hemosiderosis” refers to the deposition of ‘hemosiderin’, a storage form of Iron in the human body.

This paper reviews the literature on the treatment modalities for idiopathic pulmonary hemosiderosis (IPH) used over the past 30 years, attempting to define treatment options that appear to be efficacious and safe, and in addition presents a treatment algorithm.

Idiopathic pulmonary hemosiderosis (IPH) is a rare disease, found primarily in children, that is characterized by recurrent episodes of diffuse alveolar hemorrhage (DAH). When no underlying cause for repeated episodes of DAH is apparent (table 1), the entity is referred to as IPH [1].