Gerstmann–Sträussler–Scheinker syndrome (GSS) is an extremely rare, always fatal (due to it being caused by prions) neurodegenerative disease that affects patients from 20 to 60 years in age. It is exclusively heritable, and is found in only a few families all over the world. [ 1 ]

Gerstmann-Straussler-Scheinker disease (GSS) is an extremely rare, neurodegenerative brain disorder. It is almost always inherited and is found in only a few families around the world. The disease usually begins between the ages of 35 and 55.

Gerstmann-Straussler-Scheinker syndrome is caused by genetic mutations, also known as pathogenic variants. Genetic mutations can be hereditary, when parents pass them down to their children, or they may occur randomly when cells are dividing.

2018年7月18日 · Learn about Gerstmann-Sträussler-Scheinker Disease, including symptoms, causes, and treatments. If you or a loved one is affected by this condition, visit

Gerstmann-Sträussler-Scheinker disease (GSS) occurs worldwide and is about 100-fold less common than Creutzfeldt-Jakob disease (CJD) (1). It develops at an earlier age (40 versus 60 years), and average life expectancy is longer (5 years versus 6 months).

Gerstmann-Straussler-Scheinker disease (GSS) is an extremely rare, neurodegenerative brain disorder. It is almost always inherited and is found in only a few families around the world. Onset of the disease usually occurs between the ages of 35 and 55.

Gerstmann-Sträussler-Scheinker disease (GSS) occurs worldwide and is about 100-fold less common than Creutzfeldt-Jakob disease (CJD) (1). It develops at an earlier age (40 versus 60 years), and average life expectancy is longer (5 years versus 6 months).

Gerstmann-Straussler-Scheinker disease (GSS) is an extremely rare, neurodegenerative brain disorder. It is almost always inherited and is found in only a few families around the world. The disease usually begins between the ages of 35 and 55.

Gerstmann–Sträussler–Scheinker disease (GSS) is a rare autosomal dominant disorder characterized clinically in different families by various combinations of dementia, ataxia, pyramidal and extrapyramidal signs, and occasional amyotrophy.

Gerstmann-Sträussler-Scheinker disease is a prion disease that causes loss of coordination followed by slow deterioration of mental function. The disease is fatal, usually in about 5 years.