MAS still represents a severe and potentially fatal complication of Still’s disease. The TF recommends to be particularly vigilant for MAS with appropriate periodic blood screening and careful and tight monitoring of patients with impending MAS.

2023年9月5日 · Adult onset Still’s disease (AOSD) is a rare systemic autoinflammatory condition characterized by fever, arthralgia/ (poly)arthritis and a salmon-coloured skin rash. Other symptoms include hepatosplenomegaly, lymphadenopathy and neutrophilia [1].

2024年5月3日 · Objectives: Adult-onset Still's disease (AOSD) is a rare condition characterized by fevers, rash, and arthralgia/arthritis; most doctors treating AOSD in the Netherlands treat <5 patients per year. Currently, there is no internationally accepted treatment guideline for AOSD.

Systemic juvenile idiopathic arthritis (sJIA) and adult-onset Still's disease (AOSD) are considered the same disease, but a common approach for diagnosis and management is still missing. In May 2022, EULAR and PReS endorsed a proposal for a joint task force (TF) to develop recommendations for the diagnosis and management of sJIA and AOSD.

2024年11月14日 · Systemic juvenile idiopathic arthritis (sJIA) and adult-onset Still's disease (AOSD) are considered the same disease, but a common approach for diagnosis and management is still missing. Methods: In May 2022, EULAR and PReS endorsed a proposal for a joint task force (TF) to develop recommendations for …

2021年6月12日 · Adult-onset Still’s disease (AOSD) is a rare, but characteristic non-familial, multi-genic systemic auto-inflammatory disorder, characterized by high spiking fever, salmon-like evanescent skin rash, polyarthritis, sore throat, hyperferritinemia and leucocytosis. The hallmark of AOSD is a cytokine storm triggered by dysregulation of inflammation.

2024年9月25日 · Since 2022, EULAR and the Paediatric Rheumatology European Society (PReS) have been working to establish clinical practice guidelines for the diagnostics and management of systemic juvenile idiopathic arthritis (sJIA) and adult-onset Still’s disease (AOSD).

Background: Adult onset Still’s disease (AOSD) is a rare systemic inflammatory disorder of unknown aetiology that is responsible for a significant proportion of cases of fever of unknown origin and can also have serious musculoskeletal sequelae.

BSR's 'gold standard' clinical guidelines support evidence-based clinical practice in rheumatology. Our guidelines are developed using the methods and processes outlined in Creating Clinical Guidelines: British Society for Rheumatology Protocol …

2008年4月24日 · I've just repaired a BSR turntable for a friend. You can stack six records on it and it plays them one after the other. The sound quality leaves something to be desired though....